Lower Motor Neuron Syndrome: Proximal Arm Predominant 1,

Overview

Nosology: Also called Brachial Amyotrophic Diplegia Flail arm syndrome Vulpian-Bernhard syndrome Epidemiology Onset age: 45 to 76 years; Mean 55 years Males (79% to 90%) Sporadic Clinical Weakness: Lower motor neuron Onset Upper extremities Asymmetric: Dominant > Non-dominant side May be Distal Asymmetric (76%) Shoulder > Elbow ± Bulbar change Face & Legs: Spared for long periods Fasciculations Muscle atrophy Tendon reflexes: Reduced in arms; Preserved in legs Musculoskeletal: Subluxation of shoulder joints Progression To posterior neck & legs Respiratory failure Temporal progression Slower th

Related Conditions

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