Chronic Immune Demyelinating Neuropathies: Variants
Immune/Antibody
W
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Overview
From WUSTL Neuromuscularβ-Tubulin Ab Childhood CIDP CIDP + CNS (CCPD) Contactin-1 Ab Diabetes IgM vs GM2 & GalNAc-GD1a Motor CIDP MMN Polyradiculopathy Multifocal Upper limb M-protein IgM IgG or IgA Neurofascin Ab Onset Acute Subacute Perineuritis POEMS Sensory CIDP CISP Polyradiculopathy Multifocal CIDP 9 Nosology Multifocal CIDP Lewis-Sumner 1 MADSAM Also see: Upper limb CIDP Age range: 28 to 58 years Weakness Asymmetric Distal > Proximal Arms > Legs (78%) Proximal syndrome: Occasional Phrenic nerve: Diphragm weakness; Respiratory insufficiency Suprascapular nerve: Infraspinatus ± Supraspinatus weakness Other scatt
Related Conditions
Shared genes"Classic" Guillain-Barré Syndrome
H131GD1A
Acute Immune Polyneuropathies
GD1APATHOLOGY
Acute Motor (Axonal) Neuropathy (AMAN)
IIGQ1BGM1
ACUTE NEUROPATHIES
GD1A
Antibodies vs Glycolipids & Glycoproteins
GM1MAGGQ1B
C. Anti-GM1 Antibodies
GM1IGMGM1LMN
Classification of Acute Immune Neuropathies
GD1A
Demyelinating ataxic neuropathy with IgM binding to GalNAc-GD1a and GM2 gangliosides
GD1AACUTECHRONIC
External Resources
Data sourced from the Washington University Neuromuscular Disease Center. For clinical use, always refer to primary sources.