IMPP (Myofasciitis; EVIM) + Deafness: Enterovirus & Hypogammaglobulinemia-Related
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Overview
From WUSTL NeuromuscularEpidemiology Frequency: Rare Associations Hypogammaglobulinemia Post-Rituximab ± Ibrutinib Rx Other hypogammaglobulinemia-enterovirus syndromes: EV-D68; EV-D71 Clinical: Dermatomyopathy+ Myalgia Fatigue Strength: Often normal Tendon reflexes: Reduced Skin Rash Edema Weight loss Hearing loss Balance impairment Systemic features: More severe disease Myocarditis Enteritis, Myeloencephalitis Hepatitis Course: Progressive Treatment: IVIg Laboratory Serum CK: Normal or High Serum Aldolase: High EMG Myopathic Muscles firm on needle insertion Muscle pathology IMPP Inflammation: Especially in vascular
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Data sourced from the Washington University Neuromuscular Disease Center. For clinical use, always refer to primary sources.