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Immune & Inflammatory Myopathies: Neoplasm Associations

Immune/Antibody
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antibody/infmyop.htm#Immune & Inflammatory Myopathies: Neoplasm Associations 15

Overview

From WUSTL Neuromuscular

General Antibodies Dermatomyositis Syndromes Neoplasms Pathology Muscle Skin Polymyositis Risk Screening Immune & Inflammatory MyopathiesRisk Stratification for Neoplasm Screening High Intermediate Low IIM Subtype DM-VP, AdultRIIM BCIMDM, Amyopathic DM-VP, ChildIMPPIIM + Connective tissue diseaseIBM Clinical Feature Onset age > 40 yrsDysphagiaCutaneous necrosisTreatment resistant Males RaynaudArthropathyILD Serum Antibody Tif1-γNXP2 SAE1HMGCRMi2 MDA5Jo-1 + Ro52 Jo-1Other SynthetaseSRP54PM/Scl High Risk Patient: ≥ 2 High risk features General Risk stratification Neoplasm frequency may depend on

Related Conditions

Shared genes
Asymmetric Myopathic Weakness
VAMP
DERMATOLOGIC DISORDERS & NEUROMUSCULAR DISEASE
VP
DERMATOMYOPATHIES, IMMUNE
VP
Finger Flexion Weakness
VAMP
Granulomatous Myopathies
VAMP
Inclusion Body Myositis (IBM)
VAMPIADRB1
Inflammatory & Immune Myopathies (IIM): Acquired
RNAVAMPINCLUSION
Inflammatory Myopathy + Mitochondrial Pathology in muscle (IM-Mito), subtype of IM-VAMP
VAMP

External Resources

WUSTL Neuromuscular
Washington University Disease Center
PubMed
Biomedical Literature
GeneReviews
NCBI Expert-Authored Reviews
Orphanet
Portal for Rare Diseases
NORD
National Organization for Rare Disorders

Data sourced from the Washington University Neuromuscular Disease Center. For clinical use, always refer to primary sources.