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POEMS Syndrome

VariableImmune/AntibodyOMIM 192240
W
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antibody/pnimdem.html#POEMS Syndrome 21

Overview

From WUSTL Neuromuscular

General Laboratory Nosology Polyneuropathy Pathology Systemic Edema Endocrine Organomegaly Treatment From M. Al-Lozi POEMS: Skin Thick, Dry Clubbing of fingers From M. Al-Lozi POEMS: Edema POEMS Major diagnostic criteria: 3 needed Mandatory (2) Polyneuropathy Plasma cell proliferative disorder, Monoclonal (λ >> κ) Other (1) Vascular endothelial growth factor (VEGF): High Sclerotic bone lesions Castleman�s disease Minor diagnostic criteria: 1 needed Organomegaly Spleen, Liver; Lymph nodes Extravascular volume ↑ Edema, Pleural effusion, Ascites Endocrinopathy Adrenal, Thyroid, Pituitary, Gonadal

OMIM Entries

OMIM #192240

External Resources

WUSTL Neuromuscular
Washington University Disease Center
OMIM
Online Mendelian Inheritance in Man
PubMed
Biomedical Literature
GeneReviews
NCBI Expert-Authored Reviews
Orphanet
Portal for Rare Diseases
NORD
National Organization for Rare Disorders

Data sourced from the Washington University Neuromuscular Disease Center. For clinical use, always refer to primary sources.