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NOTALGIA PARESTHETICA

Nerve AnatomyOMIM 171400
W
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Overview

From WUSTL Neuromuscular

Anatomy: Posterior rami of spinal nerves T2 through T6 Course: Pass through multifidus spinae muscle at 90° angle course en route to epidermis Epidemiology Females: 60% to 90% Genetic associations Familial cases described MEN2A Amyloid: PLCA1 Clinical Onset ages Mean: 54 to 62 years Earlier: Familial syndromes Symptoms: Sensory Distribution Interscapular, Subscapular, Dorsal Paravertebral T2-T6 dorsal rami Itch Pain Paresthesias & Tingling Burning Hypesthesia Hypoesthesia Skin (65%) Hyperpigmented macule(s) Treatments Topical: Capsaicin; Tacrolimus; Lidocaine; Botulinum toxin; Corticosteroids

OMIM Entries

OMIM #171400OMIM #105250

Related Conditions

Shared genes
Itch: Clinical Syndromes
T6

External Resources

WUSTL Neuromuscular
Washington University Disease Center
OMIM
Online Mendelian Inheritance in Man
PubMed
Biomedical Literature
GeneReviews
NCBI Expert-Authored Reviews
Orphanet
Portal for Rare Diseases
NORD
National Organization for Rare Disorders

Data sourced from the Washington University Neuromuscular Disease Center. For clinical use, always refer to primary sources.